Presenting both historical and recent research in all aspects of fatty acid oxidation, this book forms a unique synthesis of information concerning normal and abnormal fatty acid oxidation that includes data from clinical, biochemical, and molecular studies. Fatty Acid Oxidation features a discussion of the reaction mechanisms of acyl-CoA dehydrogenases, and an examination of acyl-CoA dehydrogenase deficiencies and their relationship to sudden infant death syndrome. This diversified book also reviews diagnostic methods for identifying patients with acyl-CoA dehydrogenase defects and covers disorders of mitochondrial and peroxisomal fatty acid oxidation. Descriptions of the molecular aspects of fatty acid oxidation enzymes and studies of the molecular basis of isovaleric acidemia are also included. Describes appropriate diagnostic methods for identifying patients with metabolic disorders before they become symptomatic.